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- Publisher Website: 10.1111/1756-185X.13112
- Scopus: eid_2-s2.0-85020184698
- PMID: 28580698
- WOS: WOS:000461908400022
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Article: Spontaneous pneumomediastinum in a dermatomyositis patient with anti-melanoma differentiation-associated gene-5 antibody and interstitial lung disease despite an initial response to immunosuppressant
Title | Spontaneous pneumomediastinum in a dermatomyositis patient with anti-melanoma differentiation-associated gene-5 antibody and interstitial lung disease despite an initial response to immunosuppressant |
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Authors | |
Keywords | Dermatomyositis MDA5 Pneumomediastinum Interstitial lung disease |
Issue Date | 2019 |
Citation | International Journal of Rheumatic Diseases, 2019, v. 22 n. 3, p. 521-524 How to Cite? |
Abstract | © 2017 Asia Pacific League of Associations for Rheumatology and John Wiley & Sons Australia, Ltd. We report a 24-year-old man with anti-melanoma differentiation-associated gene-5 (MDA5) antibody-positive dermatomyositis (DM) and interstitial lung disease (ILD) who developed spontaneous pneumomediastinum. By comparing serial thoracic high-resolution computed tomography scans, we demonstrated the distinct time course showing a paradoxical occurrence of pneumomediastinum despite a radiological improvement of ILD. Our case shows that pneumomediastinum in DM can occur regardless of associated ILD and it is a serious complication that should be considered in DM patients presenting with pulmonary manifestations. Cutaneous vasculopathy may be associated with pneumomediastinum and could potentially be a useful indicator of future disease. |
Persistent Identifier | http://hdl.handle.net/10722/249161 |
ISSN | 2023 Impact Factor: 2.4 2023 SCImago Journal Rankings: 0.653 |
ISI Accession Number ID |
DC Field | Value | Language |
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dc.contributor.author | Chan, Chiu Wai Shirley | - |
dc.contributor.author | Chung, Ho Yin | - |
dc.contributor.author | Lau, Chak Sing | - |
dc.contributor.author | Tsang, Helen H.L. | - |
dc.date.accessioned | 2017-10-27T05:59:16Z | - |
dc.date.available | 2017-10-27T05:59:16Z | - |
dc.date.issued | 2019 | - |
dc.identifier.citation | International Journal of Rheumatic Diseases, 2019, v. 22 n. 3, p. 521-524 | - |
dc.identifier.issn | 1756-1841 | - |
dc.identifier.uri | http://hdl.handle.net/10722/249161 | - |
dc.description.abstract | © 2017 Asia Pacific League of Associations for Rheumatology and John Wiley & Sons Australia, Ltd. We report a 24-year-old man with anti-melanoma differentiation-associated gene-5 (MDA5) antibody-positive dermatomyositis (DM) and interstitial lung disease (ILD) who developed spontaneous pneumomediastinum. By comparing serial thoracic high-resolution computed tomography scans, we demonstrated the distinct time course showing a paradoxical occurrence of pneumomediastinum despite a radiological improvement of ILD. Our case shows that pneumomediastinum in DM can occur regardless of associated ILD and it is a serious complication that should be considered in DM patients presenting with pulmonary manifestations. Cutaneous vasculopathy may be associated with pneumomediastinum and could potentially be a useful indicator of future disease. | - |
dc.language | eng | - |
dc.relation.ispartof | International Journal of Rheumatic Diseases | - |
dc.subject | Dermatomyositis | - |
dc.subject | MDA5 | - |
dc.subject | Pneumomediastinum | - |
dc.subject | Interstitial lung disease | - |
dc.title | Spontaneous pneumomediastinum in a dermatomyositis patient with anti-melanoma differentiation-associated gene-5 antibody and interstitial lung disease despite an initial response to immunosuppressant | - |
dc.type | Article | - |
dc.description.nature | link_to_subscribed_fulltext | - |
dc.identifier.doi | 10.1111/1756-185X.13112 | - |
dc.identifier.pmid | 28580698 | - |
dc.identifier.scopus | eid_2-s2.0-85020184698 | - |
dc.identifier.hkuros | 281848 | - |
dc.identifier.volume | 22 | - |
dc.identifier.issue | 3 | - |
dc.identifier.spage | 521 | - |
dc.identifier.epage | 524 | - |
dc.identifier.eissn | 1756-185X | - |
dc.identifier.isi | WOS:000461908400022 | - |
dc.identifier.issnl | 1756-1841 | - |