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- Publisher Website: 10.1007/s00383-017-4158-4
- Scopus: eid_2-s2.0-85029759339
- PMID: 28940041
- WOS: WOS:000414503000008
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Article: A review of long-term outcome and quality of life of patients after Kasai operation surviving with native livers
Title | A review of long-term outcome and quality of life of patients after Kasai operation surviving with native livers |
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Authors | |
Keywords | Kasai operation Liver cirrhosis Quality of life Long term |
Issue Date | 2017 |
Publisher | Springer Verlag. The Journal's web site is located at http://link.springer.de/link/service/journals/00383/index.htm |
Citation | Pediatric Surgery International, 2017, v. 33 n. 12, p. 1283-1287 How to Cite? |
Abstract | Biliary atresia (BA) is a rare neonatal cholestatic disease which leads to progressive obliterative cholangiopathy, resulting in biliary obstruction and jaundice. The standard surgical treatment is hepatoportoenterostomy (Kasai operation). Although approximately 50% of the affected infants would require liver transplantation within the first 2 years of life, the other 50% of the patients can live for years with their native liver, despite the progression of cirrhosis and chronic liver disease. Many of these patients will be affected by long-term complications such as repeated cholangitis, portal hypertension, variceal bleeding, growth problems, biochemical abnormalities, and hepatic osteodystrophy. These morbidities impose a huge impact on the quality of life of the patients and their families. Herein, we performed a comprehensive review on the clinical status and quality of life of long-term survivors of biliary atresia with their native livers, to facilitate meticulous longitudinal follow-up of these patients, and alert caregivers the probable complications to be aware of. |
Persistent Identifier | http://hdl.handle.net/10722/298772 |
ISSN | 2023 Impact Factor: 1.5 2023 SCImago Journal Rankings: 0.548 |
ISI Accession Number ID |
DC Field | Value | Language |
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dc.contributor.author | Wong, KKY | - |
dc.contributor.author | Wong, CWY | - |
dc.date.accessioned | 2021-04-12T03:03:09Z | - |
dc.date.available | 2021-04-12T03:03:09Z | - |
dc.date.issued | 2017 | - |
dc.identifier.citation | Pediatric Surgery International, 2017, v. 33 n. 12, p. 1283-1287 | - |
dc.identifier.issn | 0179-0358 | - |
dc.identifier.uri | http://hdl.handle.net/10722/298772 | - |
dc.description.abstract | Biliary atresia (BA) is a rare neonatal cholestatic disease which leads to progressive obliterative cholangiopathy, resulting in biliary obstruction and jaundice. The standard surgical treatment is hepatoportoenterostomy (Kasai operation). Although approximately 50% of the affected infants would require liver transplantation within the first 2 years of life, the other 50% of the patients can live for years with their native liver, despite the progression of cirrhosis and chronic liver disease. Many of these patients will be affected by long-term complications such as repeated cholangitis, portal hypertension, variceal bleeding, growth problems, biochemical abnormalities, and hepatic osteodystrophy. These morbidities impose a huge impact on the quality of life of the patients and their families. Herein, we performed a comprehensive review on the clinical status and quality of life of long-term survivors of biliary atresia with their native livers, to facilitate meticulous longitudinal follow-up of these patients, and alert caregivers the probable complications to be aware of. | - |
dc.language | eng | - |
dc.publisher | Springer Verlag. The Journal's web site is located at http://link.springer.de/link/service/journals/00383/index.htm | - |
dc.relation.ispartof | Pediatric Surgery International | - |
dc.rights | This is a post-peer-review, pre-copyedit version of an article published in [insert journal title]. The final authenticated version is available online at: https://doi.org/[insert DOI] | - |
dc.subject | Kasai operation | - |
dc.subject | Liver cirrhosis | - |
dc.subject | Quality of life | - |
dc.subject | Long term | - |
dc.title | A review of long-term outcome and quality of life of patients after Kasai operation surviving with native livers | - |
dc.type | Article | - |
dc.identifier.email | Wong, KKY: kkywong@hku.hk | - |
dc.identifier.authority | Wong, KKY=rp01392 | - |
dc.description.nature | link_to_subscribed_fulltext | - |
dc.identifier.doi | 10.1007/s00383-017-4158-4 | - |
dc.identifier.pmid | 28940041 | - |
dc.identifier.scopus | eid_2-s2.0-85029759339 | - |
dc.identifier.hkuros | 322015 | - |
dc.identifier.volume | 33 | - |
dc.identifier.issue | 12 | - |
dc.identifier.spage | 1283 | - |
dc.identifier.epage | 1287 | - |
dc.identifier.isi | WOS:000414503000008 | - |
dc.publisher.place | Germany | - |